Hunter's syndrome: a case report.
Identifieur interne : 000169 ( Main/Exploration ); précédent : 000168; suivant : 000170Hunter's syndrome: a case report.
Auteurs : N S Savitha ; G. Saurabh [Inde] ; S H Krishnamoorthy ; S. Nandan ; A. AmbiliSource :
- Journal of the Indian Society of Pedodontics and Preventive Dentistry [ 1998-3905 ]
Descripteurs français
- KwdFr :
- MESH :
- diagnostic : Mucopolysaccharidose de type II.
- thérapie : Mucopolysaccharidose de type II.
- Adolescent, Diagnostic différentiel, Humains, Mâle.
English descriptors
- KwdEn :
- MESH :
- diagnosis : Mucopolysaccharidosis II.
- therapy : Mucopolysaccharidosis II.
- Adolescent, Diagnosis, Differential, Humans, Male.
Abstract
Hunter's syndrome or mucopolysaccharidosis (MPS) type II is an X-linked recessive mucopolysaccharide disorder caused by a defect in the metabolism of glycosaminoglycans (GAGs) characterized by involvement of nervous, cardiovascular, respiratory, and mucoskeletal systems along with numerous oral manifestations. This is a case report of a 13-year-old boy referred to the Department of Pediatric Dentistry with a chief complaint of irregularly placed teeth from a general physician. Here we highlight the pivotal role of pediatric dentists in diagnosis and treatment planning for patients diagnosed with such systemic conditions and the provision of advanced dental care in the management of the same.
DOI: 10.4103/0970-4388.149011
PubMed: 25572378
Affiliations:
Links toward previous steps (curation, corpus...)
Le document en format XML
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This is a case report of a 13-year-old boy referred to the Department of Pediatric Dentistry with a chief complaint of irregularly placed teeth from a general physician. Here we highlight the pivotal role of pediatric dentists in diagnosis and treatment planning for patients diagnosed with such systemic conditions and the provision of advanced dental care in the management of the same.</div></front></TEI><pubmed><MedlineCitation Status="MEDLINE" Owner="NLM"><PMID Version="1">25572378</PMID><DateCompleted><Year>2016</Year><Month>12</Month><Day>13</Day></DateCompleted><DateRevised><Year>2016</Year><Month>12</Month><Day>30</Day></DateRevised><Article PubModel="Print"><Journal><ISSN IssnType="Electronic">1998-3905</ISSN><JournalIssue CitedMedium="Internet"><Volume>33</Volume><Issue>1</Issue><PubDate><MedlineDate>2015 Jan-Mar</MedlineDate></PubDate></JournalIssue><Title>Journal of the Indian Society of Pedodontics and Preventive Dentistry</Title><ISOAbbreviation>J Indian Soc Pedod Prev Dent</ISOAbbreviation></Journal><ArticleTitle>Hunter's syndrome: a case report.</ArticleTitle><Pagination><MedlinePgn>66-8</MedlinePgn></Pagination><ELocationID EIdType="doi" ValidYN="Y">10.4103/0970-4388.149011</ELocationID><Abstract><AbstractText>Hunter's syndrome or mucopolysaccharidosis (MPS) type II is an X-linked recessive mucopolysaccharide disorder caused by a defect in the metabolism of glycosaminoglycans (GAGs) characterized by involvement of nervous, cardiovascular, respiratory, and mucoskeletal systems along with numerous oral manifestations. This is a case report of a 13-year-old boy referred to the Department of Pediatric Dentistry with a chief complaint of irregularly placed teeth from a general physician. 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Ambili</name><name sortKey="Krishnamoorthy, S H" sort="Krishnamoorthy, S H" uniqKey="Krishnamoorthy S" first="S H" last="Krishnamoorthy">S H Krishnamoorthy</name><name sortKey="Nandan, S" sort="Nandan, S" uniqKey="Nandan S" first="S" last="Nandan">S. Nandan</name><name sortKey="Savitha, N S" sort="Savitha, N S" uniqKey="Savitha N" first="N S" last="Savitha">N S Savitha</name></noCountry><country name="Inde"><noRegion><name sortKey="Saurabh, G" sort="Saurabh, G" uniqKey="Saurabh G" first="G" last="Saurabh">G. Saurabh</name></noRegion></country></tree></affiliations></record>Pour manipuler ce document sous Unix (Dilib)
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